Kaposiform Hemangioendothelioma with Kasabach-Merritt Syndrome

Kaposiform hemangioendothelioma is a rare, aggressive vascular skin, tissue and bone tumor found in children. It’s characterized by nodules and sheets of spindle cells that become warped in the extremities, chest and abdomen causing the blood vessels to expand. Although a relatively rare condition, the increasing number of reports on kaposiform hemangioendothelioma in infants and children is often complicated by rapidly growing lesions, also known as Kasabach-Merritt syndrome (KMS).